Meat borne Prion disease
Bovine Spongiform Encephalopathy(BSE) and varient Creutzfeldt-Jacob disease
It is chronic and fatal Prion disease. These prions are undestroyable even by a temperature of 350°C. BSE belongs to Transmissible Spongiform Encepahopathy (TSE). In humans, it is known as Creutzfeldt-Jacob disease, in sheep, it is called Scrapie. The disease has been reported throughout Europe. The disease is transmitted through BSE contaminated meat, and bone meal supplements in cattle feed. Removal of specific risk materials (brain, spinal cord) from the carcass during dressing operations, appropriate handling of nervous tissues and lymph nodes of the carcass suspected to be infected with BSE and appropriate disposal of suspected/infected carcass comes under prevention.
Kuru disease
Kuru is among the fatal neurodegenerative prion protein (PrP) diseases in humans. Fore people who practised cannabalism at past, by eating cooked and consumed body parts(brain and viscera) of their family members following their death to symbolize respect and mourning suffered from this disease. Also ingestion of prion particles cause this disease. It causes physiological and neurological effects which ultimately lead to death. It is characterized by progressive cerebellar ataxia, or loss of coordination and control over muscle movements. he symptoms of the disease include muscle twitching and loss of coordination. Other symptoms include difficulty walking, involuntary movements, behavioral and mood changes, dementia, and difficulty eating. The latter can cause malnutrition. Kuru has no known cure. It’s usually fatal within one year of contraction.